Authors
Alekseev K.I., Vetshev F.P., Pavlova E.A., Petukhova N.V., Tertychny A.S.
M. Sechenov First Moscow State Medical University, Moscow
Abstract
Abrikossoff’s tumor is a rare benign tumor originating from Schwann cells. It accounts for 1% of all benign esophageal tumors and has a potential for malignancy. Even small tumors (<10 mm) can be malignant. At the N.N. Burdenko Central Clinical Hospital of the I.M. Sechenov First Moscow State Medical University, endoscopic submucosal dissection) was performed on 4 patients with granular cell tumors (GCT) of the esophagus <20 mm. ESD is the preferred method for removing tumors up to 30 mm. For very small tumors (<10 mm), EMR (endoscopic mucosal resection) can be used; for tumors 20-30 mm in size, especially with signs of invasion into the muscular layer, submucosal tunneling endoscopic resection (STER) is an option. Surgical treatment is indicated for tumors >35 mm and/or signs of invasion into the muscular layer. Due to the risk of malignancy and the need to differentiate them from other malignant submucosal neoplasms, such as GIST, esophageal GCTs should be removed. The choice of treatment method depends on the tumor’s size, location, and depth of invasion, as determined by endoscopic ultrasound.
Keywords: еsophagus, granular cell tumor, Abrikossoff’s tumor, endoscopic submucosal dissection.
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