DOI: 10.25881/20728255_2022_17_4_2_146


Ablitsov A.Y., Levchuk A.L., Ablitsov Y.A., Lovtsevich N.V., Plotnitskiy A.V., Shepetkova L.V., Sharova I.O., Suslov R.P.

Pirogov National Medical and Surgical Center, Moscow


A case of successful surgical treatment of a patient with a giant solitary fibrous pleural tumor is presented in a clinical observation. The Doege-Potter syndrome and Pierre Marie-Bamberger syndrome, one of the manifestations of which are changes in the fingers of the «drumsticks» type, and hypoglycemia, are paraneoplastic syndromes characteristic of solitary fibrous pleural tumors (SFPT). SFPT are extremely rare. It is even rarer to find in the literature descriptions of patients with both benign and malignant SFPT and paraneoplastic syndromes, and all the authors have experience of 1–2 operations. The patient underwent a lower lobectomy on the left along with the bulk of the tumor. The operation was accompanied by massive blood loss. The postoperative period was difficult and was accompanied by complications. However, at the control examination after 8 months, the condition is satisfactory. There were no attacks of hypoglycemia after surgery, the fingers of the hands changed. No recurrence or metastasis of the tumor was detected during X-ray examination.

Keywords: zase report, Doege–Potter syndrome, hypoglycemia, solitary fibrous tumor.


1. Pishchik VG, Obornev AD, Zinchenko EI, SHibinbekov NR. Gigantskie solitarnye fibroznye opuholi plevry: obzor literatury i sobstvennyj opyt. Klinicheskaya bol’nica. 2016; 2(16): 66-80. (In Russ.)

2. Ryabov AB, Pikin OV, Abu-Hajdar OB. Zlokachestvennyj variant solitarnoj fibroznoj opuholi plevry so stojkoj gipoglikemiej: klinicheskoe nablyudenie. Sibirskij onkologicheskij zhurnal. 2020; 19(2): 147-152. (In Russ.)

3. Fernández-Trujillo L, Bolaños JE, Álvarez C, Giraldo J, Velásquez M, Zúñiga-Restrepo V, Pérez B, Sua LF. Doege-Potter Syndrome and Hypoglycemia associated with Solitary Fibrous Tumor of the Pleura: Two Case Reports. Clin Med Insights Circ Respir Pulm Med. 2020; Oct 13;14.

4. Han G, Zhang Z, Shen X, Wang K, Zhao Y, He J, et al. Doege-Potter syndrome: A review of the literature including a new case report. Medicine (Baltimore). 2017; 96(27): e 741.

5. Kalebi AY, Hale MJ, Wong ML, Hoffman T, Murray J. Surgically cured hypoglycemia secondary to pleural solitary fibrous tumour: case report and update review on the Doege-Potter syndrome. Ann. Cardiothorac Surg. 2009; 4: 45.

6. Kelin Y, Lvcong Z, Liang W, Ruiming X, Jianfeng Y, Wenbin H, Zhongqiang Y. Resection of giant malignant solitary fibrous pleural tumor after interventional embolization: a case report and literature review. J. Cardiothoracic Surgery. 2022; 1717: 134.

7. Solsi A, Pho K, Shojaie S, Findakly D, Noori T. Doege-Potter Syndrome and Pierre-Marie-Bamberger Syndrome in a Patient With Pleural Solitary Fibrous Tumor: A Rare Case With Literature Review. Cureus. 2020; 12(5): e7919.

8. Wen Meng, Hong-Hong Zhu, Hu Li, Guoqing Wang, Dongshan Wei, Xing Feng. Solitary fibrous tumors of the pleura with Doege-Potter syndrome: a case report and three-decade review of the literature BMC Res Notes. 2014; 7: 515.

For citation

Ablitsov A.Y., Levchuk A.L., Ablitsov Y.A., Lovtsevich N.V., Plotnitskiy A.V., Shepetkova L.V., Sharova I.O., Suslov R.P. Doege-Potter and Pierre Marie-Bamberger syndromes in a patient with a giant solitary fibrous of the pleura. Bulletin of Pirogov National Medical & Surgical Center. 2022;17(4-2):146-149. (In Russ.)