DOI: 10.25881/20728255_2023_18_4_S1_80

Authors

Davletshina L.M 1, 2, Zagidullina A.Sh.1, Batyrshin R.A.1

1 Bashkir State Medical University, Ufa

2 Clinical Emergency Hospital, Ufa

Abstract

The Sturge-Weber syndrome presented in the article in a 54 year old woman is a clinical case of sporadic encephalotrigeminal angiomatosis with ophthalmological manifestations in the form of secondary open-angle glaucoma, detected at a late stage. Primary treatment with complaints from the organ of vision made it possible to be set the main diagnosis and prescribe local antihypertensive and general syndromic treatment.

Keywords: Sturge-Weber syndrome, secondary glaucoma, phakomatosis, encephalotrigeminal angiomatosis, case report.

References

1. Gasanova K.M., Zagidullina A.Sh., Enikeeva R.T. Atypical form of Sturge-Weber-Krabbe (Lawford) syndrome // Medical Bulletin of Bashkortostan 2015;10(2): p.141-145. (In Russ)

2. Basinsky V.A., Gorbunova E.A., Nevgen D.V. About Sturge-Weber syndrome // Journal of the Grodno State Medical University 2010;1:p103–104. (In Russ)

3. Olshanskaya A.S., Schneider N.A., Dmitrenko D.V., Kozina E.V., Chesheiko E.Yu., Ilyenkov S.S., Tsuprikova M.E. Damage to the organ of vision in Sturge-Weber syndrome // ENI Transbaikal Medical Bulletin 2017;2: p.196-203. (In Russ)

For citation

Davletshina L.M , Zagidullina A.Sh., Batyrshin R.A. Ophthalmological manifestations of Sturge-Weber syndrome. Bulletin of Pirogov National Medical & Surgical Center. 2023;18(4,supplement):80-81. (In Russ.) https://doi.org/10.25881/20728255_2023_18_4_S1_80